Caroli´s syndrome confined to the left hepatic duct. The
disease manifested with jaandice at the age of
28. The left hepatic duct is dilated sac- like on the left
x-ray after extraction of multiple stones.
Right: The left hepatic duct is still considerably dilated
after 6 weeks. Liver biopsy fails to show
changes. Classic Caroli´s syndrome is a rare autosomal-
recessive disorder with sac- like, segmental dilatation of
biliary tree with concomitant concrements. Hepatic blood
vessels may be affected in the same way.